Definition

Moyamoya Angiopathy

Encompasses both Moyamoya Disease and Moyamoya Syndrome

The word “Moyamoya”: Japanese word meaning “puff of smoke” describing the network of new vessel formation as a compensation to the decreased blood flow in both the brain hemispheres due to obstruction of the two main brain vessels the internal carotid arteries.

Commonly used terms:

Moyamoya Disease, Moyamoya Syndrome, Cerebral revascularisation

• Moyamoya disease: presence of obstruction (stenosis/occlusion) of the two main brain arteries the internal carotid arteries ICA within the skull vault (intracranially) on the angiography. Additional presence of new vessel formation/Moyamoya network of vessels.
• Moyamoya Syndrome: presence of other systemic diseases along with the intracranial Moyamoya findings.
• Cerebral/Brain revascularisation: to revascularise or to supply additional blood flow to brain areas with low flow due to obstruction of brain vessels/arteries